Six adult patients with septo-optic dysplasia and drug-resistant epilepsy: Clinical findings and course☆☆☆★★★☆☆☆
نویسندگان
چکیده
Septo-optic dysplasia (SOD) is a rare disorder associated with optic nerve hypoplasia, pituitary abnormalities and agenesis/dysgenesis of midline brain structures including the septum pellucidum and corpus callosum. Though sometimes associated with drug-resistant epilepsy, this association has not been well studied. We report six SOD patients with associated malformation of cortical development (MCD) and drug-resistant epilepsy who underwent video-EEG telemetry at our centre between 1998 and 2016 for drug-resistant epilepsy. Three then underwent surgery; right temporal neocortical resection, right functional hemispherectomy and placement of a vagus nerve stimulator. Clinical findings and the patients' ultimate courses are discussed.
منابع مشابه
رابطه متغیرهای بالینی صرع با عملکرد شناختی و آشفتگی هیجانی در بیماران مبتلا به صرع مقاوم به دارو
Background & Aims: Issues in patients with drug-resistant epilepsy are important due to their impact on quality of life and the course of the disease. The purpose of this study was to investigate the relationship between epileptic clinical variables with cognitive function and emotional disturbance in patients with drug-resistant epilepsy. Materials & Methods: This descriptive correlational st...
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